The sparing of extraocular muscle in dystrophinopathy is lost in mice lacking utrophin and dystrophin

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				M. H. J. Wiesen, S. Bogdanovich, I. Agarkova, J.-C. Perriard, and T. S. Khurana Identification and Characterization of Layer-Specific Differences in Extraocular Muscle M-Bands Invest. Ophthalmol. Vis. Sci., March 1, 2007; 48(3): 1119 - 1127. [Abstract] [Full Text] [PDF]

				R. Kafri, M. Levy, and Y. Pilpel The regulatory utilization of genetic redundancy through responsive backup circuits PNAS, August 1, 2006; 103(31): 11653 - 11658. [Abstract] [Full Text] [PDF]

				K. A. Kleopa, A. Drousiotou, E. Mavrikiou, A. Ormiston, and T. Kyriakides Naturally occurring utrophin correlates with disease severity in Duchenne muscular dystrophy Hum. Mol. Genet., May 15, 2006; 15(10): 1623 - 1628. [Abstract] [Full Text] [PDF]

				J. D. Porter, S. Israel, B. Gong, A. P. Merriam, J. Feuerman, S. Khanna, and H. J. Kaminski Distinctive morphological and gene/protein expression signatures during myogenesis in novel cell lines from extraocular and hindlimb muscle Physiol Genomics, February 23, 2006; 24(3): 264 - 275. [Abstract] [Full Text] [PDF]

				H. Yin, J. S. Stahl, F. H. Andrade, C. A. McMullen, S. Webb-Wood, N. J. Newman, V. Biousse, D. C. Wallace, and M. T. Pardue Eliminating the Ant1 Isoform Produces a Mouse with CPEO Pathology but Normal Ocular Motility Invest. Ophthalmol. Vis. Sci., December 1, 2005; 46(12): 4555 - 4562. [Abstract] [Full Text] [PDF]

				M. D. Fischer, M. T. Budak, M. Bakay, J. R. Gorospe, D. Kjellgren, F. Pedrosa-Domellof, E. P. Hoffman, and T. S. Khurana Definition of the unique human extraocular muscle allotype by expression profiling Physiol Genomics, August 11, 2005; 22(3): 283 - 291. [Abstract] [Full Text] [PDF]

				A. Yamane, S. Akutsu, T. G. H. Diekwisch, and R. Matsuda Satellite cells and utrophin are not directly correlated with the degree of skeletal muscle damage in mdx mice Am J Physiol Cell Physiol, July 1, 2005; 289(1): C42 - C48. [Abstract] [Full Text] [PDF]

				S. Khanna, G. Cheng, B. Gong, M. J. Mustari, and J. D. Porter Genome-Wide Transcriptional Profiles Are Consistent with Functional Specialization of the Extraocular Muscle Layers Invest. Ophthalmol. Vis. Sci., September 1, 2004; 45(9): 3055 - 3066. [Abstract] [Full Text] [PDF]

				G. Cheng, A. P. Merriam, B. Gong, P. Leahy, S. Khanna, and J. D. Porter Conserved and muscle-group-specific gene expression patterns shape postnatal development of the novel extraocular muscle phenotype Physiol Genomics, July 8, 2004; 18(2): 184 - 195. [Abstract] [Full Text] [PDF]

				J. D. Porter, A. P. Merriam, P. Leahy, B. Gong, J. Feuerman, G. Cheng, and S. Khanna Temporal gene expression profiling of dystrophin-deficient (mdx) mouse diaphragm identifies conserved and muscle group-specific mechanisms in the pathogenesis of muscular dystrophy Hum. Mol. Genet., February 1, 2004; 13(3): 257 - 269. [Abstract] [Full Text] [PDF]

				J. D. Porter, A. P. Merriam, B. Gong, S. Kasturi, X. Zhou, K. F. Hauser, F. H. Andrade, and G. Cheng Postnatal suppression of myomesin, muscle creatine kinase and the M-line in rat extraocular muscle J. Exp. Biol., September 1, 2003; 206(17): 3101 - 3112. [Abstract] [Full Text] [PDF]

				F. H. Andrade, A. P. Merriam, W. Guo, G. Cheng, C. A. McMullen, K. Hayess, P. F. M. van der Ven, and J. D. Porter Paradoxical absence of M lines and downregulation of creatine kinase in mouse extraocular muscle J Appl Physiol, August 1, 2003; 95(2): 692 - 699. [Abstract] [Full Text] [PDF]

				S. Khanna, C. R. Richmonds, H. J. Kaminski, and J. D. Porter Molecular Organization of the Extraocular Muscle Neuromuscular Junction: Partial Conservation of and Divergence from the Skeletal Muscle Prototype Invest. Ophthalmol. Vis. Sci., May 1, 2003; 44(5): 1918 - 1926. [Abstract] [Full Text] [PDF]

				M. D. Fischer, J. R. Gorospe, E. Felder, S. Bogdanovich, F. Pedrosa-Domellof, R. S. Ahima, N. A. Rubinstein, E. P. Hoffman, and T. S. Khurana Expression profiling reveals metabolic and structural components of extraocular muscles Physiol Genomics, May 10, 2002; 9(2): 71 - 84. [Abstract] [Full Text] [PDF]

				I. N. Rybakova, J. R. Patel, K. E. Davies, P. D. Yurchenco, and J. M. Ervasti Utrophin Binds Laterally along Actin Filaments and Can Couple Costameric Actin with Sarcolemma When Overexpressed in Dystrophin-deficient Muscle Mol. Biol. Cell, May 1, 2002; 13(5): 1512 - 1521. [Abstract] [Full Text] [PDF]

				G. Cheng and J. D. Porter Transcriptional Profile of Rat Extraocular Muscle by Serial Analysis of Gene Expression Invest. Ophthalmol. Vis. Sci., April 1, 2002; 43(4): 1048 - 1058. [Abstract] [Full Text] [PDF]

				D. J. Blake, A. Weir, S. E. Newey, and K. E. Davies Function and Genetics of Dystrophin and Dystrophin-Related Proteins in Muscle Physiol Rev, April 1, 2002; 82(2): 291 - 329. [Abstract] [Full Text] [PDF]

				W. Irwin, E. Fontaine, L. Agnolucci, D. Penzo, R. Betto, S. Bortolotto, C. Reggiani, G. Salviati, and P. Bernardi Bupivacaine Myotoxicity Is Mediated by Mitochondria J. Biol. Chem., March 29, 2002; 277(14): 12221 - 12227. [Abstract] [Full Text] [PDF]

				M. Sussman Duchenne Muscular Dystrophy J. Am. Acad. Ortho. Surg., March 1, 2002; 10(2): 138 - 151. [Abstract] [Full Text] [PDF]

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				R. H. Crosbie, C. S. Lebakken, K. H. Holt, D. P. Venzke, V. Straub, J. C. Lee, R. M. Grady, J. S. Chamberlain, J. R. Sanes, and K. P. Campbell Membrane Targeting and Stabilization of Sarcospan Is Mediated by the Sarcoglycan Subcomplex J. Cell Biol., April 5, 1999; 145(1): 153 - 165. [Abstract] [Full Text] [PDF]