The Emery-Dreifuss muscular dystrophy phenotype arises from aberrant targeting and binding of emerin at the inner nuclear membrane

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				C. L. Stewart, K. J. Roux, and B. Burke Blurring the Boundary: The Nuclear Envelope Extends Its Reach Science, November 30, 2007; 318(5855): 1408 - 1412. [Abstract] [Full Text] [PDF]

				N. Leach, S. L. Bjerke, D. K. Christensen, J. M. Bouchard, F. Mou, R. Park, J. Baines, T. Haraguchi, and R. J. Roller Emerin Is Hyperphosphorylated and Redistributed in Herpes Simplex Virus Type 1-Infected Cells in a Manner Dependent on both UL34 and US3 J. Virol., October 1, 2007; 81(19): 10792 - 10803. [Abstract] [Full Text] [PDF]

				A. Muchir, P. Pavlidis, G. Bonne, Y. K. Hayashi, and H. J. Worman Activation of MAPK in hearts of EMD null mice: similarities between mouse models of X-linked and autosomal dominant Emery Dreifuss muscular dystrophy Hum. Mol. Genet., August 1, 2007; 16(15): 1884 - 1895. [Abstract] [Full Text] [PDF]

				J. B. Morris, H. Hofemeister, and P. O'Hare Herpes Simplex Virus Infection Induces Phosphorylation and Delocalization of Emerin, a Key Inner Nuclear Membrane Protein J. Virol., May 1, 2007; 81(9): 4429 - 4437. [Abstract] [Full Text] [PDF]

				J. M. Holaska, S. Rais-Bahrami, and K. L. Wilson Lmo7 is an emerin-binding protein that regulates the transcription of emerin and many other muscle-relevant genes Hum. Mol. Genet., December 1, 2006; 15(23): 3459 - 3472. [Abstract] [Full Text] [PDF]

				R. Ozawa, Y. K. Hayashi, M. Ogawa, R. Kurokawa, H. Matsumoto, S. Noguchi, I. Nonaka, and I. Nishino Emerin-Lacking Mice Show Minimal Motor and Cardiac Dysfunctions with Nuclear-Associated Vacuoles Am. J. Pathol., March 1, 2006; 168(3): 907 - 917. [Abstract] [Full Text] [PDF]

				Y. Hirano, M. Segawa, F. S. Ouchi, Y. Yamakawa, K. Furukawa, K. Takeyasu, and T. Horigome Dissociation of Emerin from Barrier-to-autointegration Factor Is Regulated through Mitotic Phosphorylation of Emerin in a Xenopus Egg Cell-free System J. Biol. Chem., December 2, 2005; 280(48): 39925 - 39933. [Abstract] [Full Text] [PDF]

				T. Libotte, H. Zaim, S. Abraham, V. C. Padmakumar, M. Schneider, W. Lu, M. Munck, C. Hutchison, M. Wehnert, B. Fahrenkrog, et al. Lamin A/C-dependent Localization of Nesprin-2, a Giant Scaffolder at the Nuclear Envelope Mol. Biol. Cell, July 1, 2005; 16(7): 3411 - 3424. [Abstract] [Full Text] [PDF]

				F. Lin, J. M. Morrison, W. Wu, and H. J. Worman MAN1, an integral protein of the inner nuclear membrane, binds Smad2 and Smad3 and antagonizes transforming growth factor-{beta} signaling Hum. Mol. Genet., February 1, 2005; 14(3): 437 - 445. [Abstract] [Full Text] [PDF]

				H. Hofemeister and P. O'Hare Analysis of the Localization and Topology of Nurim, a Polytopic Protein Tightly Associated with the Inner Nuclear Membrane J. Biol. Chem., January 28, 2005; 280(4): 2512 - 2521. [Abstract] [Full Text] [PDF]

				K. Z. Al-Shali and R. A. Hegele Laminopathies and Atherosclerosis Arterioscler Thromb Vasc Biol, September 1, 2004; 24(9): 1591 - 1595. [Abstract] [Full Text] [PDF]

				B. R. Johnson, R. T. Nitta, R. L. Frock, L. Mounkes, D. A. Barbie, C. L. Stewart, E. Harlow, and B. K. Kennedy A-type lamins regulate retinoblastoma protein function by promoting subnuclear localization and preventing proteasomal degradation PNAS, June 29, 2004; 101(26): 9677 - 9682. [Abstract] [Full Text] [PDF]

				I. Holt, C. Ostlund, C. L. Stewart, N. t. Man, H. J. Worman, and G. E. Morris Effect of pathogenic mis-sense mutations in lamin A on its interaction with emerin in vivo J. Cell Sci., July 15, 2003; 116(14): 3027 - 3035. [Abstract] [Full Text] [PDF]

				S. S. Mani, R. Rajagopal, A. B. Garfinkel, X. Fan, and M. F. Wolfner A hydrophilic lamin-binding domain from the Drosophila YA protein can target proteins to the nuclear envelope J. Cell Sci., May 15, 2003; 116(10): 2067 - 2072. [Abstract] [Full Text] [PDF]

				C. Vigouroux, M. Auclair, E. Dubosclard, M. Pouchelet, J. Capeau, J.-C. Courvalin, and B. Buendia Nuclear envelope disorganization in fibroblasts from lipodystrophic patients with heterozygous R482Q/W mutations in the lamin A/C gene J. Cell Sci., March 14, 2002; 114(24): 4459 - 4468. [Abstract] [Full Text] [PDF]

				Q. Zhang, J. N. Skepper, F. Yang, J. D. Davies, L. Hegyi, R. G. Roberts, P. L. Weissberg, J. A. Ellis, and C. M. Shanahan Nesprins: a novel family of spectrin-repeat-containing proteins that localize to the nuclear membrane in multiple tissues J. Cell Sci., March 14, 2002; 114(24): 4485 - 4498. [Abstract] [Full Text] [PDF]

				K. K. Lee, T. Haraguchi, R. S. Lee, T. Koujin, Y. Hiraoka, and K. L. Wilson Distinct functional domains in emerin bind lamin A and DNA-bridging protein BAF J. Cell Sci., March 14, 2002; 114(24): 4567 - 4573. [Abstract] [Full Text] [PDF]

				T. Haraguchi, T. Koujin, M. Segura-Totten, K. K. Lee, Y. Matsuoka, Y. Yoneda, K. L. Wilson, and Y. Hiraoka BAF is required for emerin assembly into the reforming nuclear envelope J. Cell Sci., March 14, 2002; 114(24): 4575 - 4585. [Abstract] [Full Text] [PDF]

				Bh. Muralikrishna, J. Dhawan, N. Rangaraj, and V. K. Parnaik Distinct changes in intranuclear lamin A/C organization during myoblast differentiation J. Cell Sci., March 13, 2002; 114(22): 4001 - 4011. [Abstract] [Full Text] [PDF]

				O. A. Vaughan, M. Alvarez-Reyes, J. M. Bridger, J. L. V. Broers, F. C. S. Ramaekers, M. Wehnert, G. E. Morris, W. G. F. Whitfield, and C. J. Hutchison Both emerin and lamin C depend on lamin A for localization at the nuclear envelope J. Cell Sci., March 9, 2002; 114(14): 2577 - 2590. [Abstract] [Full Text] [PDF]

				E. A. L. Fairley, A. Riddell, J. A. Ellis, and J. Kendrick-Jones The cell cycle dependent mislocalisation of emerin may contribute to the Emery-Dreifuss muscular dystrophy phenotype J. Cell Sci., January 15, 2002; 115(2): 341 - 354. [Abstract] [Full Text] [PDF]

				Y. Gruenbaum, K. K. Lee, J. Liu, M. Cohen, and K. L. Wilson The expression, lamin-dependent localization and RNAi depletion phenotype for emerin in C. elegans J. Cell Sci., January 3, 2002; 115(5): 923 - 929. [Abstract] [Full Text] [PDF]

				J. M. K. Mislow, M. S. Kim, D. B. Davis, and E. M. McNally Myne-1, a spectrin repeat transmembrane protein of the myocyte inner nuclear membrane, interacts with lamin A/C J. Cell Sci., January 1, 2002; 115(1): 61 - 70. [Abstract] [Full Text] [PDF]

				E. C. Schirmer, T. Guan, and L. Gerace Involvement of the Lamin Rod Domain in Heterotypic Lamin Interactions Important for Nuclear Organization J. Cell Biol., April 30, 2001; 153(3): 479 - 490. [Abstract] [Full Text] [PDF]

				S. Boyle, S. Gilchrist, J. M. Bridger, N. L. Mahy, J. A. Ellis, and W. A. Bickmore The spatial organization of human chromosomes within the nuclei of normal and emerin-mutant cells Hum. Mol. Genet., February 1, 2001; 10(3): 211 - 219. [Abstract] [Full Text] [PDF]

				C. Hutchison, M Alvarez-Reyes, and O. Vaughan Lamins in disease: why do ubiquitously expressed nuclear envelope proteins give rise to tissue-specific disease phenotypes? J. Cell Sci., January 1, 2001; 114(1): 9 - 19. [Abstract] [PDF]

				M. Izumi, O. A. Vaughan, C. J. Hutchison, and D. M. Gilbert Head and/or CaaX Domain Deletions of Lamin Proteins Disrupt Preformed Lamin A and C But Not Lamin B Structure in Mammalian Cells Mol. Biol. Cell, December 1, 2000; 11(12): 4323 - 4337. [Abstract] [Full Text]

				K. K. Lee, Y. Gruenbaum, P. Spann, J. Liu, and K. L. Wilson C. elegans Nuclear Envelope Proteins Emerin, MAN1, Lamin, and Nucleoporins Reveal Unique Timing of Nuclear Envelope Breakdown during Mitosis Mol. Biol. Cell, September 1, 2000; 11(9): 3089 - 3099. [Abstract] [Full Text]

				T Haraguchi, T Koujin, T Hayakawa, T Kaneda, C Tsutsumi, N Imamoto, C Akazawa, J Sukegawa, Y Yoneda, and Y Hiraoka Live fluorescence imaging reveals early recruitment of emerin, LBR, RanBP2, and Nup153 to reforming functional nuclear envelopes J. Cell Sci., January 3, 2000; 113(5): 779 - 794. [Abstract] [PDF]

				T. Sullivan, D. Escalante-Alcalde, H. Bhatt, M. Anver, N. Bhat, K. Nagashima, C. L. Stewart, and B. Burke Loss of a-Type Lamin Expression Compromises Nuclear Envelope Integrity Leading to Muscular Dystrophy J. Cell Biol., November 29, 1999; 147(5): 913 - 920. [Abstract] [Full Text] [PDF]